Lambert-Eaton myasthenic syndrome

Lambert-Eaton myasthenic syndrome

Definition

Lambert-Eaton myasthenic syndrome (LEMS) is an autoimmune, presynaptic disorder of neuromuscular transmission characterized by fluctuating muscle weakness and autonomic dysfunction frequently associated with small-cell lung cancer (SCLC).

Also known as Eaton Lambert syndrome, Eaton-Lambert syndrome, Lambert Eaton myasthenic syndrome, Lambert Eaton syndrome, Lambert-Eaton syndrome, myasthenic syndrome of Lambert-Eaton, myasthenic-myopathic syndrome of Lambert-Eaton — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Musculature Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculature Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Nervous system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Nervous system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Peripheral nervous system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Peripheral nervous system Disease Has Primary Anatomic Site NCIT · CC BY 4.0

Drugs indicated

Drug Relation Source
Amifampridine may treat MEDRT · Public domain (U.S. Government work)