Ewing sarcoma of bone

Definition

A small round cell bone tumor that lacks morphologic, immunohistochemical, and electron microscopic evidence of neuroectodermal differentiation. It represents one of the two ends of the spectrum called Ewing sarcoma/peripheral neuroectodermal tumor. It often affects the diaphysis or metaphyseal-diaphyseal portion of long bones. Clinical findings include pain and a mass in the involved area. fever, anemia, leukocytosis, and an increased sedimentation rate are often seen. X-ray examination reveals osteolytic lesions. The prognosis depends on the stage, anatomic location, and size of the tumor.

Also known as bone Ewing's sarcoma, bone localised Ewing sarcoma, bone localised Ewing's sarcoma, bone tissue Ewing sarcoma, Ewing sarcoma of bone, Ewing's sarcoma of bone, Ewing's sarcoma, osseous, Ewing's sarcoma/bone peripheral primitive neuroectodermal tumour, localised skeletal Ewing's sarcoma, osseous Ewing's sarcoma, osseous Ewing's tumor, osseous Ewing's tumour, skeletal Ewing's sarcoma, skeletal Ewing's tumor, skeletal Ewing's tumour — per MONDO

Also identified as

• DOID 3368 per MONDO
• ICD9 170.9 per MONDO
• NCIT C4835 per MONDO
• SCTID 307608006 per MONDO
• UMLS C0585474 per MONDO

Affected Organs