Hypoplastic left heart syndrome

Definition

Hypoplastic left heart syndrome (HLHS) refers to the abnormal development of the left-sided cardiac structures, resulting in obstruction to blood flow from the left ventricular outflow tract. In addition, the syndrome includes underdevelopment of the left ventricle, aorta, and aortic arch, as well as mitral atresia or stenosis.

Also known as HLHS — per MONDO

Also identified as

• DOID 9955 per MONDO
• ICD10CM Q23.4 per MONDO
• ICD9 746.7 per MONDO
• MESH D018636 per MONDO
• NCIT C98894 per MONDO
• Orphanet 2248 per MONDO
• SCTID 62067003 per MONDO
• UMLS C0152101 per MONDO

Drugs indicated