Leiomyosarcoma
Leiomyosarcoma
Definition
An uncommon, aggressive malignant smooth muscle neoplasm, usually occurring in post-menopausal women. It is characterized by a proliferation of neoplastic spindle cells. Morphologic variants include epithelioid, granular cell, inflammatory and myxoid leimyosarcomas.
Also known as leiomyosarcoma, leiomyosarcoma - not uterine, leiomyosarcoma (excluding uterine leiomyosarcoma), leiomyosarcoma, malignant, Leiomyosarcomas — per MONDO
Also identified as
- DOID 1967 per MONDO
- ICD9 171.9 per MONDO
- MESH D007890 per MONDO
- NCIT C3158 per MONDO
- Orphanet 64720 per MONDO
- SCTID 443719001 per MONDO
- UMLS C0023269 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Smooth muscle | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Trabectedin | may treat | MEDRT · Public domain (U.S. Government work) |