Hereditary multiple osteochondromas
Hereditary multiple osteochondromas
Definition
A bone neoplasm characterized by development of two or more cartilage capped bony outgrowths (osteochondromas) of the long bones.
Also known as Bessel-Hagen disease, exostoses, multiple, multiple cartilaginous exostoses, osteochondromatosis syndrome, osteochondromatosis syndrome (disorder) [ambiguous] — per MONDO
Also identified as
- DOID 206 per MONDO
- MESH D005097 per MONDO
- NCIT C5183 per MONDO
- Orphanet 321 per MONDO
- SCTID 254044004 per MONDO
- SCTID 716742001 per MONDO
- UMLS C0015306 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone element | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Bone element | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Connective tissue | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Connective tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |