Fibrous dysplasia
Fibrous dysplasia
Definition
A genetic, non-inheritable disorder caused by osteoblastic differentiation defects that result in the replacement of bone marrow and trabecular bone by fibrous stroma and immature bone. It usually affects a single bone and less frequently multiple bones. Skull, femur, tibia, and humerus are the most frequently affected bones. It manifests with pain, deformities, and fractures.
Also known as fibrous dysplasia of bone — per MONDO
Also identified as
- DOID 0080031 per MONDO
- ICD9 733.29 per MONDO
- MESH D005357 per MONDO
- NCIT C34609 per MONDO
- Orphanet 249 per MONDO
- SCTID 10623005 per MONDO
- SCTID 254145001 per MONDO
- UMLS C0259779 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone element | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Bone element | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Connective tissue | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |