Morgagni-Stewart-Morel syndrome
Morgagni-Stewart-Morel syndrome
Definition
Morgagni-Stewart-Morel syndrome is characterized by thickening of the inner table of the frontal bone, sometimes associated with obesity and hypertrichosis. It mainly affects women over 35 years of age. The prevalence and clinical significance of hyperostosis frontalis interna is unknown. Transmission is either X-linked or autosomal dominant.
Also known as Hyperostosis Frontalis Interna, Morgagni-Stewart-Morel syndrome — per MONDO
Also identified as
- MESH D006957 per MONDO
- NCIT C84772 per MONDO
- OMIM 144800 per MONDO
- Orphanet 77296 per MONDO
- SCTID 82054006 per MONDO
- UMLS C0020494 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone element | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Bone element | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Connective tissue | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |