Extramammary Paget disease

Definition

A malignant neoplasm in which there is infiltration of the skin by neoplastic large cells with abundant pale cytoplasm and large nuclei with prominent nucleoli (Paget cells). It may affect the anus, penis, scrotum, and vulva.

Also known as extramammary Paget disease, Extramammary Paget's disease, Paget disease Extramammary, Paget's disease of skin, Paget's disease of the skin, Paget's skin disease — per MONDO

Also identified as

• MESH D010145 per MONDO
• NCIT C3302 per MONDO
• OMIM 167300 per MONDO
• Orphanet 2800 per MONDO
• UMLS C0030186 per MONDO

Drugs indicated