Polyostotic fibrous dysplasia
ICD-10 Code
Q78.1
Polyostotic fibrous dysplasia
Definition
Fibrous dysplasia affecting more than one bone. When it is associated with café-au-lait skin pigmentation and endocrine disorders, it is known as McCune-Albright syndrome.
Also known as PFD, polyostotic fibrous dysplasia of bone — per MONDO
Also identified as
- ICD10CM Q78.1 per MONDO
- ICD9 756.54 per MONDO
- MESH D005359 per MONDO
- NCIT C34610 per MONDO
- Orphanet 93276 per MONDO
- SCTID 36517007 per MONDO
- UMLS C0016065 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone element | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Bone element | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Connective tissue | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |