Acquired polycythemia vera
ICD-10 Code
D45
Acquired polycythemia vera
Definition
Polycythemia vera (PV) is an acquired myeloproliferative disorder characterized by an elevated absolute red blood cell mass caused by uncontrolled red blood cell production, frequently associated with uncontrolled white blood cell and platelet production.
Also known as acquired primary erythrocytosis, Osler-Vaquez disease, polycythaemia rubra vera, polycythemia rubra vera, polycythemia vera, polycythemia vera, somatic, PV, Vaquez disease — per MONDO
Also identified as
- DOID 8997 per MONDO
- ICD10CM D45 per MONDO
- ICD9 238.4 per MONDO
- MESH D011087 per MONDO
- NCIT C3336 per MONDO
- OMIM 263300 per MONDO
- Orphanet 729 per MONDO
- UMLS C0032463 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone marrow | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Bone marrow | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Anagrelide | may treat | MEDRT · Public domain (U.S. Government work) |
| Busulfan | may treat | MEDRT · Public domain (U.S. Government work) |
| Hydroxyurea | may treat | MEDRT · Public domain (U.S. Government work) |
| Ropeginterferon Alfa-2B | may treat | MEDRT · Public domain (U.S. Government work) |
| Ruxolitinib | may treat | MEDRT · Public domain (U.S. Government work) |