X-linked dominant hypophosphatemic rickets

X-linked dominant hypophosphatemic rickets

Definition

X-linked hypophosphatemia (XLH) is a hereditary renal phosphate-wasting disorder characterized by hypophosphatemia, rickets and/or osteomalacia, and diminished growth.

Also known as hereditary hypophosphatemic rickets, X-linked, hypophosphatemic rickets, X-linked, hypophosphatemic rickets, X-linked dominant, X-linked dominant, rickets, vitamin D-resistant, vitamin D-resistant rickets, X-linked, X-linked dominant hypophosphatemic rickets, X-linked hereditary hypophosphatemic rickets, XLH — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Bone element Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Bone element Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Connective tissue Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0