Pulmonary fibrosis

ICD-10 Code J84
Category Respiratory

Pulmonary fibrosis

Definition

Chronic progressive interstitial lung disorder characterized by the replacement of the lung tissue by connective tissue, leading to progressive dyspnea, respiratory failure, or right heart failure. Causes include chronic inflammatory processes, exposure to environmental irritants, radiation therapy, autoimmune disorders, certain drugs, or it may be idiopathic (no identifiable cause).

Also known as pulmonary interstitial fibrosis — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Lungs Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Lungs Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Respiratory system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Respiratory system Disease Has Primary Anatomic Site NCIT · CC BY 4.0

Drugs indicated

Drug Relation Source
Oxygen may treat MEDRT · Public domain (U.S. Government work)
Pirfenidone may treat MEDRT · Public domain (U.S. Government work)