Osteofibrous dysplasia

Osteofibrous dysplasia

Definition

A benign, usually self-limited fibro-osseous lesion of the bone that affects infants and children. It usually arises from the cortical bone of the anterior mid-shaft of the tibia. Patients usually present with swelling or painless bowing of the tibia. Progression to adamantinoma has been reported in some cases.

Also known as cortical fibrous dysplasia, Kempson-Campanacci lesion, OFD, OSFD, ossifying fibroma of long bones, osteofibrous dysplasia, osteofibrous dysplasia of bone, tibia, bowing of, with pseudarthrosis and pectus excavatum — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Bone element Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Bone element Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Connective tissue Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Musculoskeletal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0