Osteofibrous dysplasia
Osteofibrous dysplasia
Definition
A benign, usually self-limited fibro-osseous lesion of the bone that affects infants and children. It usually arises from the cortical bone of the anterior mid-shaft of the tibia. Patients usually present with swelling or painless bowing of the tibia. Progression to adamantinoma has been reported in some cases.
Also known as cortical fibrous dysplasia, Kempson-Campanacci lesion, OFD, OSFD, ossifying fibroma of long bones, osteofibrous dysplasia, osteofibrous dysplasia of bone, tibia, bowing of, with pseudarthrosis and pectus excavatum — per MONDO
Also identified as
- MESH C563276 per MONDO
- MESH C563787 per MONDO
- NCIT C53970 per MONDO
- OMIM 607278 per MONDO
- OMIM 609143 per MONDO
- Orphanet 488265 per MONDO
- UMLS C4085248 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone element | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Bone element | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Connective tissue | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |