Sezary syndrome
Sezary syndrome
Definition
Sezary syndrome (SS) is an aggressive form of cutaneous T-cell lymphoma characterized by a triad of erythroderma, lymphadenopathy and circulating atypical lymphocytes (Sezary cells).
Also known as CTCL / Sezary syndrome, cutaneous T-cell lymphoma/Sezary syndrome, SC)zary syndrome, Sezary disease, Sezary lymphoma, Sezary syndrome, Sezary's disease — per MONDO
Also identified as
- DOID 8541 per MONDO
- ICD9 202.2 per MONDO
- MESH D012751 per MONDO
- NCIT C3366 per MONDO
- Orphanet 3162 per MONDO
- SCTID 118611004 per MONDO
- UMLS C0036920 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone marrow | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Hematopoietic system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Skin of body | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Interferon Alfa-N3 | may treat | MEDRT · Public domain (U.S. Government work) |
| Interferon Beta-1B | may treat | MEDRT · Public domain (U.S. Government work) |
| Interferon Gamma-1b | may treat | MEDRT · Public domain (U.S. Government work) |
| Mogamulizumab | may treat | MEDRT · Public domain (U.S. Government work) |
| Peginterferon Alfa-2a | may treat | MEDRT · Public domain (U.S. Government work) |