Huntington's disease
ICD-10 Code
G10
Category
Neurological
Huntington's disease
Definition
Huntington disease (HD) is a rare neurodegenerative disorder of the central nervous system characterized by unwanted choreatic movements, behavioral and psychiatric disturbances and dementia.
Also known as HD, Huntington chorea, Huntington disease, Huntington's chorea, Huntington's Disease — per MONDO
Also identified as
- DOID 12858 per MONDO
- ICD10CM G10 per MONDO
- ICD9 333.4 per MONDO
- MESH D006816 per MONDO
- NCIT C82342 per MONDO
- OMIM 143100 per MONDO
- Orphanet 399 per MONDO
- SCTID 58756001 per MONDO
- UMLS C0020179 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Baclofen | may treat | MEDRT · Public domain (U.S. Government work) |
| Coenzyme Q10 | may treat | MEDRT · Public domain (U.S. Government work) |
| Perphenazine | may treat | MEDRT · Public domain (U.S. Government work) |
| Pimozide | may treat | MEDRT · Public domain (U.S. Government work) |